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Date Published: 26/09/2022
Abstract Views: 112
Views PDF: 112
DOI: https://doi.org/10.60117/vjmap.v46i5.59
Issue
Vol. 46 No. 5 (2022)
Section
Research Articles
How to Cite
Trịnh, T. H., Bùi, T. T. Q., Nguyễn, T. L., Hoàng, K. K., Lê, H. T., Lê, Q. C., Nguyễn, T. V. A., & Nguyễn, V. K. (2022). Quality Of Life Of The Primary Immunodeficiency Disease Patients. Viet Nam Journal of Traditional Medicine and Pharmacy, 46(5), 32-37. https://doi.org/10.60117/vjmap.v46i5.59

Quality Of Life Of The Primary Immunodeficiency Disease Patients

Thị Hậu Trịnh, Thị Thúy Quỳnh Bùi, Thị Lan Nguyễn, Kim Khanh Hoàng, Huyền Trang Lê, Quỳnh Chi Lê, Thị Vân Anh Nguyễn, Văn Khiêm Nguyễn

Main Article Content

Abstract

Primary immunodeficiency is a group of heterogeneous genetic diseases characterized by disorder of immuno- system, which greatly affects the quality of life (QoL) of patients.


Objectives: Investigating the quality of life of children with primary immunodeficiency by using Ped QL 4.


Method: A cross sectional-study, using the quality of life for children Peds QL 4.0, was implemented to investigate the quality of life of 52 children diagnosed with primary immunodeficiency.


Results:The ratio of male/female was 6/1, average age was 7,2 ± 4,0, patients aged 2-4 ranked highest with 38,5%. Among them, patients with lymphoid B were 63,5%, patients with phagocytosis disorder were 23,1%,


patients with complex type were 23,1%. The QoL score in terms of studying of patients aged 13-18 was higher than the rest of patients (p = 0,01< 0,05). The QoL related to studying, physical health and total score of patients with lymphoid B were higher than the other types of primary immunodeficiency (p < 0,05). The QoL related to studying, physical health and total score of primary immunodeficiency patients were lower than those of healthy children (p < 0,05).


Conclusion: The QoL related to studying, physical health and total score of primary immunodeficiency patients were signigicantly lower than those of healthy children. It is neccesary to evaluate the QoL of primary immunodeficiency patients at different times and longer duration after treatment.

Article Details

Keywords

Children, primary immunodeficiency, quality of life.

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